Glandular odontogenic cyst: insights into a rare and challenging lesion.
The glandular odontogenic cyst (GOC) is a rare developmental odontogenic cyst characterized by an epithelial lining resembling salivary or glandular tissue. Its aggressive behavior and potential for recurrence pose challenges in both diagnosis and management. This review consolidates current knowled...
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| Muut tekijät: | , , , , , |
| Aineistotyyppi: | article |
| Kieli: | englanti |
| Julkaistu: |
2025
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| Aiheet: | |
| Linkit: | https://hdl.handle.net/20.500.12008/51892 |
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| _version_ | 1868890080703152128 |
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| author | Schuch, Lauren Frenzel |
| author2 | Silveira, Felipe Martins González Umpiérrez, María Natalia Beovide Cortegoso, Verónica Sicco, Estefanía Bologna-Molina, Ronell Pereira-Prado, Vanesa |
| author2_role | author author author author author author |
| author_browse | Beovide Cortegoso, Verónica Bologna-Molina, Ronell González Umpiérrez, María Natalia Pereira-Prado, Vanesa Schuch, Lauren Frenzel Sicco, Estefanía Silveira, Felipe Martins |
| author_facet | Schuch, Lauren Frenzel Silveira, Felipe Martins González Umpiérrez, María Natalia Beovide Cortegoso, Verónica Sicco, Estefanía Bologna-Molina, Ronell Pereira-Prado, Vanesa |
| author_role | author |
| collection | COLIBRI |
| dc.contributor.none.fl_str_mv | Schuch Lauren Frenzel, Universidad de la República (Uruguay). Facultad de Odontología. Departamento de Diagnóstico en Patología y Medicina Oral. Silveira Felipe Martins, Universidad de la República (Uruguay). Facultad de Odontología. Departamento de Diagnóstico en Patología y Medicina Oral. González Umpiérrez María Natalia, Universidad de la República (Uruguay). Facultad de Odontología. Departamento de Diagnóstico en Patología y Medicina Oral. Beovide Cortegoso Verónica, Universidad de la República (Uruguay). Facultad de Odontología. Departamento de Diagnóstico en Patología y Medicina Oral. Sicco Estefanía, Universidad de la República (Uruguay). Facultad de Odontología. Departamento de Diagnóstico en Patología y Medicina Oral. Bologna-Molina Ronell, Universidad de la República (Uruguay). Facultad de Odontología. Departamento de Diagnóstico en Patología y Medicina Oral. Pereira-Prado Vanesa, Universidad de la República (Uruguay). Facultad de Odontología. Departamento de Diagnóstico en Patología y Medicina Oral. |
| dc.creator.none.fl_str_mv | Schuch, Lauren Frenzel Silveira, Felipe Martins González Umpiérrez, María Natalia Beovide Cortegoso, Verónica Sicco, Estefanía Bologna-Molina, Ronell Pereira-Prado, Vanesa |
| dc.date.none.fl_str_mv | 2025-10-03T17:54:37Z 2025-10-03T17:54:37Z 2025 |
| dc.format.none.fl_str_mv | 6 h. application/pdf |
| dc.identifier.none.fl_str_mv | Schuch, L, Silveira, F, González Umpiérrez, M, [y otros autores]. "Glandular odontogenic cyst: insights into a rare and challenging lesion". Journal of Oral Diagnosis. [en línea] 2025, 10:e292. 2525-5711 https://hdl.handle.net/20.500.12008/51892 10.5327/2525-5711.292 |
| dc.language.none.fl_str_mv | en_US eng |
| dc.publisher.none.fl_str_mv | Brazilian Society of Oral Medicine and Oral Pathology (SOBEP). |
| dc.relation.none.fl_str_mv | Journal of Oral Diagnosis, 2025, 10:e292. |
| dc.rights.none.fl_str_mv | info:eu-repo/semantics/openAccess Licencia Creative Commons Atribución (CC - By 4.0) |
| dc.source.none.fl_str_mv | reponame:COLIBRI instname:Universidad de la República instacron:Universidad de la República |
| dc.subject.none.fl_str_mv | Odontogenic lesion Glandular odontogenic cyst Diagnostic challenge QUISTES ODONTOGÉNICOS ODONTOGENIC CYSTS |
| dc.title.none.fl_str_mv | Glandular odontogenic cyst: insights into a rare and challenging lesion. |
| dc.type.none.fl_str_mv | Artículo info:eu-repo/semantics/article info:eu-repo/semantics/publishedVersion |
| description | The glandular odontogenic cyst (GOC) is a rare developmental odontogenic cyst characterized by an epithelial lining resembling salivary or glandular tissue. Its aggressive behavior and potential for recurrence pose challenges in both diagnosis and management. This review consolidates current knowledge on etiopathogenesis, clinical presentation, histopathological features, and treatment approaches. GOC primarily affects male adults, often presenting asymptomatically, and is most commonly found in the mandible. Radiographically, it appears as a unilocular or multilocular radiolucency, frequently associated with unerupted teeth. Histologically, GOC is istinguished by a multilocular cystic structure lined with epithelial cells, which may include “hobnail,” clear, and mucous cells. While traditionally thought to lack MAML2 gene rearrangements, recent studies have identified MAML2 fusion transcripts in recurrent GOCs, suggesting a link to aggressive behavior. The differential diagnosis includes both benign and malignant conditions. Treatment options range from conservative management to radical resection, with recurrence being a notable concern. This review highlights the need for accurate diagnosis and long-term follow-up, as no histopathological features reliably predict recurrence. Further research is needed to optimize treatment strategies and deepen understanding of its biological behavior. |
| eu_rights_str_mv | openAccess |
| format | article |
| id | anni_65a2bac91afa2b8d84c96c8b7ce9bf36 |
| identifier_str_mv | Schuch, L, Silveira, F, González Umpiérrez, M, [y otros autores]. "Glandular odontogenic cyst: insights into a rare and challenging lesion". Journal of Oral Diagnosis. [en línea] 2025, 10:e292. 2525-5711 10.5327/2525-5711.292 |
| instacron_str | Universidad de la República |
| institution | Universidad de la República |
| instname_str | Universidad de la República |
| language | eng |
| language_invalid_str_mv | en_US |
| network_acronym_str | anni |
| network_name_str | oai-lr-anni |
| oai_identifier_str | oai:colibri.udelar.edu.uy:20.500.12008/51892 |
| publishDate | 2025 |
| publishDateSort | 2025 |
| publisher.none.fl_str_mv | Brazilian Society of Oral Medicine and Oral Pathology (SOBEP). |
| reponame_str | COLIBRI |
| repository.mail.fl_str_mv | |
| repository.name.fl_str_mv | |
| repository_id_str | |
| rights_invalid_str_mv | Licencia Creative Commons Atribución (CC - By 4.0) |
| spelling | Glandular odontogenic cyst: insights into a rare and challenging lesion.Schuch, Lauren FrenzelSilveira, Felipe MartinsGonzález Umpiérrez, María NataliaBeovide Cortegoso, VerónicaSicco, EstefaníaBologna-Molina, RonellPereira-Prado, VanesaOdontogenic lesionGlandular odontogenic cystDiagnostic challengeQUISTES ODONTOGÉNICOSODONTOGENIC CYSTSThe glandular odontogenic cyst (GOC) is a rare developmental odontogenic cyst characterized by an epithelial lining resembling salivary or glandular tissue. Its aggressive behavior and potential for recurrence pose challenges in both diagnosis and management. This review consolidates current knowledge on etiopathogenesis, clinical presentation, histopathological features, and treatment approaches. GOC primarily affects male adults, often presenting asymptomatically, and is most commonly found in the mandible. Radiographically, it appears as a unilocular or multilocular radiolucency, frequently associated with unerupted teeth. Histologically, GOC is istinguished by a multilocular cystic structure lined with epithelial cells, which may include “hobnail,” clear, and mucous cells. While traditionally thought to lack MAML2 gene rearrangements, recent studies have identified MAML2 fusion transcripts in recurrent GOCs, suggesting a link to aggressive behavior. The differential diagnosis includes both benign and malignant conditions. Treatment options range from conservative management to radical resection, with recurrence being a notable concern. This review highlights the need for accurate diagnosis and long-term follow-up, as no histopathological features reliably predict recurrence. Further research is needed to optimize treatment strategies and deepen understanding of its biological behavior.Brazilian Society of Oral Medicine and Oral Pathology (SOBEP).Schuch Lauren Frenzel, Universidad de la República (Uruguay). Facultad de Odontología. Departamento de Diagnóstico en Patología y Medicina Oral.Silveira Felipe Martins, Universidad de la República (Uruguay). Facultad de Odontología. Departamento de Diagnóstico en Patología y Medicina Oral.González Umpiérrez María Natalia, Universidad de la República (Uruguay). Facultad de Odontología. Departamento de Diagnóstico en Patología y Medicina Oral.Beovide Cortegoso Verónica, Universidad de la República (Uruguay). Facultad de Odontología. Departamento de Diagnóstico en Patología y Medicina Oral.Sicco Estefanía, Universidad de la República (Uruguay). Facultad de Odontología. Departamento de Diagnóstico en Patología y Medicina Oral.Bologna-Molina Ronell, Universidad de la República (Uruguay). Facultad de Odontología. Departamento de Diagnóstico en Patología y Medicina Oral.Pereira-Prado Vanesa, Universidad de la República (Uruguay). Facultad de Odontología. Departamento de Diagnóstico en Patología y Medicina Oral.2025-10-03T17:54:37Z2025-10-03T17:54:37Z2025Artículoinfo:eu-repo/semantics/articleinfo:eu-repo/semantics/publishedVersion6 h.application/pdfSchuch, L, Silveira, F, González Umpiérrez, M, [y otros autores]. "Glandular odontogenic cyst: insights into a rare and challenging lesion". Journal of Oral Diagnosis. [en línea] 2025, 10:e292.2525-5711https://hdl.handle.net/20.500.12008/5189210.5327/2525-5711.292reponame:COLIBRIinstname:Universidad de la Repúblicainstacron:Universidad de la Repúblicaen_USengJournal of Oral Diagnosis, 2025, 10:e292.Las obras depositadas en el Repositorio se rigen por la Ordenanza de los Derechos de la Propiedad Intelectual de la Universidad de la República.(Res. Nº 91 de C.D.C. de 8/III/1994 – D.O. 7/IV/1994) y por la Ordenanza del Repositorio Abierto de la Universidad de la República (Res. Nº 16 de C.D.C. de 07/10/2014)info:eu-repo/semantics/openAccessLicencia Creative Commons Atribución (CC - By 4.0)oai:colibri.udelar.edu.uy:20.500.12008/518922026-04-14T10:37:16Z |
| spellingShingle | Glandular odontogenic cyst: insights into a rare and challenging lesion. Schuch, Lauren Frenzel Odontogenic lesion Glandular odontogenic cyst Diagnostic challenge QUISTES ODONTOGÉNICOS ODONTOGENIC CYSTS |
| status_str | publishedVersion |
| title | Glandular odontogenic cyst: insights into a rare and challenging lesion. |
| title_full | Glandular odontogenic cyst: insights into a rare and challenging lesion. |
| title_fullStr | Glandular odontogenic cyst: insights into a rare and challenging lesion. |
| title_full_unstemmed | Glandular odontogenic cyst: insights into a rare and challenging lesion. |
| title_short | Glandular odontogenic cyst: insights into a rare and challenging lesion. |
| title_sort | Glandular odontogenic cyst: insights into a rare and challenging lesion. |
| topic | Odontogenic lesion Glandular odontogenic cyst Diagnostic challenge QUISTES ODONTOGÉNICOS ODONTOGENIC CYSTS |
| url | https://hdl.handle.net/20.500.12008/51892 |